Research supported by MLC

The MLC supports the work of many research groups across a diverse range of disease areas, including hearing loss, type 2 diabetes, sex determination, neurodegeneration and circadian function, to name a few. Such support can include detailed phenotyping in addition to generation and husbandry of mutant mouse lines.

Cinacalcet corrects hypercalcemia in mice with an inactivating Galpha11 mutation

Howles, S. A., Hannan, F. M., Gorvin, C. M., Piret, S. E., Paudyal, A., Stewart, M., Hough, T. A., Nesbit, M. A., Wells, S., Brown, S. D., Cox, R. D., Thakker, R. V.

(2017) , JCI Insight , 2 , e96540

10.1172/jci.insight.96540

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Biallelic Variants in OTUD6B Cause an Intellectual Disability Syndrome Associated with Seizures and Dysmorphic Features

Santiago-Sim, T., Burrage, L. C., Ebstein, F., Tokita, M. J., Miller, M., Bi, W., Braxton, A. A., Rosenfeld, J. A., Shahrour, M., Lehmann, A., Cogne, B., Kury, S., Besnard, T., Isidor, B., Bezieau, S., Hazart, I., Nagakura, H., Immken, L. L., Littlejohn, R. O., Roeder, E., Kara, B., Hardies, K., Weckhuysen, S., May, P., Lemke, J. R., Elpeleg, O., Abu-Libdeh, B., James, K. N., Silhavy, J. L., Issa, M. Y., Zaki, M. S., Gleeson, J. G., Seavitt, J. R., Dickinson, M. E., Ljungberg, M. C., Wells, S., Johnson, S. J., Teboul, L., Eng, C. M., Yang, Y., Kloetzel, P. M., Heaney, J. D., Walkiewicz, M. A.

(2017) , Am J Hum Genet , 100 , 676-688

10.1016/j.ajhg.2017.03.001

PMC5384096

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A mutation in Nischarin causes otitis media via LIMK1 and NF-kappaB pathways

Crompton, M., Purnell, T., Tyrer, H. E., Parker, A., Ball, G., Hardisty-Hughes, R. E., Gale, R., Williams, D., Dean, C. H., Simon, M. M., Mallon, A. M., Wells, S., Bhutta, M. F., Burton, M. J., Tateossian, H., Brown, S. D. M.

(2017) , PLoS Genet , 13 , e1006969

10.1371/journal.pgen.1006969

PMC5570507

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Mice with an N-Ethyl-N-Nitrosourea (ENU) Induced Tyr209Asn Mutation in Natriuretic Peptide Receptor 3 (NPR3) Provide a Model for Kyphosis Associated with Activation of the MAPK Signaling Pathway

Esapa, C. T., Piret, S. E., Nesbit, M. A., Loh, N. Y., Thomas, G., Croucher, P. I., Brown, M. A., Brown, S. D., Cox, R. D., Thakker, R. V.

(2016) , PLoS One , 11 , e0167916

10.1371/journal.pone.0167916

PMC5570507

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Loss-of-Function Mutations in FRRS1L Lead to an Epileptic-Dyskinetic Encephalopathy

Madeo, M., Stewart, M., Sun, Y., Sahir, N., Wiethoff, S., Chandrasekar, I., Yarrow, A., Rosenfeld, J. A., Yang, Y., Cordeiro, D., McCormick, E. M., Muraresku, C. C., Jepperson, T. N., McBeth, L. J., Seidahmed, M. Z., El Khashab, H. Y., Hamad, M., Azzedine, H., Clark, K., Corrochano, S., Wells, S., Elting, M. W., Weiss, M. M., Burn, S., Myers, A., Landsverk, M., Crotwell, P. L., Waisfisz, Q., Wolf, N. I., Nolan, P. M., Padilla-Lopez, S., Houlden, H., Lifton, R., Mane, S., Singh, B. B., Falk, M. J., Mercimek-Mahmutoglu, S., Bilguvar, K., Salih, M. A., Acevedo-Arozena, A., Kruer, M. C.

(2016) , Am J Hum Genet , 98 , 1249-55

10.1016/j.ajhg.2016.04.008

Pmc4908178

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